28 April 2009
Tracheoesophageal fistula and severe esophageal stenosis in a patient with Behçet’s disease. Report of a case and literature review
Konstantinos Tsalis, Konstantinos Blouhos, Leonidas Sakkas, Emmanouel Christoforidis, Charalampos LazaridisAm J Case Rep 2009; 10:47-51 :: ID: 869649
Abstract
Background: In Adamandiades-Behçet’s Disease (ABD), controversy has existed over the incidence of esophageal involvement, which may be a direct threat to the patient’s life.
Case Report: We describe a case of tracheoesophageal fistula after stent placement in a 50-year-old female with ABD. The onset of ABD was typical. For the last three years she complained of diffi culty in swallowing both solid and liquid foods. Endoscopy revealed ulcerative esophagitis and a markedly stenotic
esophagus in the middle and distal portion. She was on a treatment regime including immunosuppressivetherapy. Balloon and bougie dilations were necessary to relieve her symptoms.After an additional episode of restenosis, an esophageal stent was placed, but her clinical course was complicated with a tracheoesophageal fistula. The patient was taken to the operating room where a right thoracotomy was performed. The fistula was dissected free, and the tracheal defect was closed with a two-layer esophageal poutch and with a rotated diaphragmatic flap, based on a well-vascularized pericardiophrenic pedicle. Staged reconstruction of the alimentary continuity was planed. The postoperative course complicated with severe haemorrhage from the chest tube. A second look operation was performed to identify and control the bleeding sources. Unfortunately, the patient died during her transfer from the theatre to the ICU.
Conclusions: All ABD patients should be evaluated for esophageal involvement. Although selected ABD patients with esophageal stenosis may benefit with temporary stenting, we believe that in patients with a persisting fistula track or in the presence of severe symptoms surgical intervention with a tailored approach is inevitable.
Keywords: esophageal involvement, Behçet’s disease, Adamandiades-Behçet’s disease, Tracheoesophageal Fistula, esophageal stenting
In Press
14 Mar 2024 : Case report
Pathogenic Potential of a PCK1 Gene Variant in Cytosolic PEPCK Deficiency: A Compelling Case StudyAm J Case Rep In Press; DOI: 10.12659/AJCR.943118
14 Mar 2024 : Case report
Management of Nontraumatic Spontaneous Renal Hemorrhage (Wünderlich Syndrome) through Robotic-Assisted Lapa...Am J Case Rep In Press; DOI: 10.12659/AJCR.942826
14 Mar 2024 : Case report
Simultaneous Occurrence of Collagen Type III Glomerulopathy and Immunoglobulin A Nephropathy: A Rare Case R...Am J Case Rep In Press; DOI: 10.12659/AJCR.942770
16 Mar 2024 : Case report
Castleman Disease Presenting in the Neck: A Report of 3 Cases and a Literature ReviewAm J Case Rep In Press; DOI: 10.12659/AJCR.943214
Most Viewed Current Articles
07 Mar 2024 : Case report
Neurocysticercosis Presenting as Migraine in the United StatesDOI :10.12659/AJCR.943133
Am J Case Rep 2024; 25:e943133
10 Jan 2022 : Case report
A Report on the First 7 Sequential Patients Treated Within the C-Reactive Protein Apheresis in COVID (CACOV...DOI :10.12659/AJCR.935263
Am J Case Rep 2022; 23:e935263
19 Jul 2022 : Case report
Atlantoaxial Subluxation Secondary to SARS-CoV-2 Infection: A Rare Orthopedic Complication from COVID-19DOI :10.12659/AJCR.936128
Am J Case Rep 2022; 23:e936128
23 Feb 2022 : Case report
Penile Necrosis Associated with Local Intravenous Injection of CocaineDOI :10.12659/AJCR.935250
Am J Case Rep 2022; 23:e935250